‘Vanishing carpal bones’ in a patient with congenital adrenal hyperplasia – A diagnostic dilemma

Document Type

Article

Publication Title

Journal of Orthopaedics

Abstract

The vanishing bone disease, also known as Gorhams disease usually involves long bones. Isolated carpal bone involvement is uncommon. A 14 year old male presented with pain in the right wrist joint since 4 months. He was a known case of Congenital Adrenal Hyperplasia on oral steroids for 3 years. X-rays showed deformed arthritic scaphoid, lunate and capitate. A proximal row carpectomy was performed to provide functional wrist mobility to the patient. Histopathological examination was consistent with Gorham's disease. In a patient with systemic disease receiving steroid therapy Gorhams disease poses a diagnostic challenge.

First Page

493

Last Page

496

DOI

10.1016/j.jor.2020.10.001

Publication Date

11-1-2020

This document is currently not available here.

Share

COinS